ABSTRACT
Apresentamos o caso de uma paciente de 34 anos com quadro sugestivo de síndrome de Susac ou vasculopatia retinococlear. Esta síndrome, descrita pela primeira vez em 1979, caracteriza-se pela presença de uma tríade clínica formada por encefalopatia, hipoacusia neurossensorial e alteraçöes visuais. A fisiopatologia ainda é controversa, assim como o tratamento de escolha. Devido a tratar-se de enfermidade insuficientemente conhecida em nosso meio, onde näo foi relatada ainda, chamamos a atençäo para o diagnóstico diferencial, que inclui condiçöes como esclerose múltipla, vasculites do sistema nervoso central e outros transtornos vasculares
Subject(s)
Humans , Female , Adult , Brain Diseases/diagnosis , Hearing Loss, Sensorineural/diagnosis , Retinal Artery Occlusion/diagnosis , SyndromeABSTRACT
Forty-four patients with neuritic leprosy were individually followed for periods ranging from 4 months to almost 4 years for the purpose of ascertaining the presence and/ or absence of leprosy. The neural symptoms presented were sensory impairment (41), parasthesia (28), nerve enlargement (22), nerve tenderness (20), paresia (20), amyotrophy (8). Leprosy was diagnosed in ten out of the total number of patients studied. Leprosy was confirmed by the appearance of reactional neuritis (4), reversal reaction (2), biopsy of the hypoesthesic area (3) and the appearance of non-reactional cutaneous lesion. We reported an experience in the diagnosis of neuritic leprosy and its most frequent clinical presentation with which clinicians have to be acquainted. We can also state that the clinical follow-up was an effective strategy for the diagnosis of the disease when diagnostic facilities are not available or have not confirmed the diagnosis
Subject(s)
Humans , Female , Adult , Middle Aged , Leprosy/diagnosis , Neuritis/diagnosis , Peripheral Nervous System Diseases/complications , Follow-Up Studies , Leprosy/etiology , Neuritis/etiologyABSTRACT
Os autores registram um caso de paraplegia causada por uma lesao granulomatosa de PCM intramedular. O diagnostico clinico neurologico de uma lesao compressiva intramedular foi confirmado pelo exame de ressonancia nuclear magnetica da coluna, que mostrou lesao captante de contraste a nivel de T12. O paciente foi operado e a lesao totalmente retirada. O exame histopatologico da peca operatoria confirmou o diagnostico de PCM. O doente esta em uso de SMZ/TMP e fluconazol com boa recuperacao neurologica
